Quick Answer: How Common Are Infantile Spasms?

Are infantile spasms dangerous?

Infantile spasms is a complex and rare disorder that can have very serious consequences.

It can lead to death in some babies, and cause intellectual disabilities and developmental problems in others.

Even once the seizures are gone, the damaging brain effects can remain..

At what age do infantile spasms start?

Infantile spasms (also known as West syndrome) is a form of epilepsy that occurs in 1 in 2,000 children. It typically begins between 2-12 months of age and peaks between 4-8 months of age.

What is the best treatment for infantile spasms?

Treatment of infantile spasms has little class I data, but adrenocorticotropic hormone (ACTH), prednisolone and vigabatrin have the best evidence as first-line medications. Other therapies including the ketogenic diet and other anti-epileptics medications may also prove useful in the treatment of infantile spasms.

How often do infantile spasms occur?

Infantile spasms are not common. It affects around one out of three thousand infants. In about 20 percent of cases, the cause is not known.

How do I know if my baby has infantile spasms?

Symptoms of Infantile Spasms (IS)Raise their arms over their head or stick their arms straight out to the side.Stiffen their legs or “tuck them into the belly,” as if having stomach pain.Suddenly bend at the waist.Drop or bob their heads briefly.Roll their eyes back suddenly with subtle head nodding.More items…

Can infantile spasm be cured?

Many children with infantile spasms develop other kinds of epilepsy. (Watch examples of infantile spasms.) “Some of these children can be cured, but successful treatment often depends on prompt diagnosis,” said Hussain.

Do infantile spasms show up on EEG?

Infantile spasms are a very specific type of seizure with a characteristic age of onset (a typical age when seizures start). They are nearly always accompanied by a very characteristic pattern on the electroencephalogram (EEG). This pattern is called ‘hypsarrhythmia’.

Do infantile spasms cause mental retardation?

Infantile spasms (IS), i.e., West syndrome, as an epileptic encephalopathy, represents one of the major causes of acquired mental retardation in early childhood (Roger and Dulac, 1994).

Do infantile spasms occur daily?

In between clusters of spasms many hours without spasms can occur. Occasionally more than a day will pass without a cluster of spasms. Clusters of spasms often occur after waking from sleep, whatever time of the day. When an infant has a typical spasm, there are several movements.

Are baby spasms normal?

Expect some of the following: Sudden jerks or twitches of the arms, hands or legs. If they only occur during sleep, they are most likely normal. How Long: last a few seconds, but can recur.

What is infant shudder syndrome?

Shuddering attacks are benign nonepileptic events that typically begin in infancy. The clinical events consist of rapid shivering of the head, shoulder, and occasionally the trunk. As in our patient, events have been reported as brief, usually lasting not more than a few seconds.

What does seizure look like in baby?

Focal seizures: Focal seizures may involve the infant having spasms or rigidity in one muscle group, becoming pale, sweating, vomiting, screaming, crying, gagging, smacking their lips, or becoming unconscious. For an example of how a focal seizure might look, click here.

What are the signs to look for in neurological symptoms in infants?

Warning signs of neurological disordersAbnormal muscle tone at birth.Seizures.Floppy baby.Subtle staring/unresponsive episodes.Slow language and/or motor skills.Decrease in developmental milestones.

Can babies grow out of infantile spasms?

They look very much like a startle. Babies also might have slowed development or loss of skills (like babbling, sitting, or crawling). Although the spasms usually go away by the time a child is 4 years old, many babies with IS will have other kinds of epilepsy later in life.

Do infantile spasms hurt?

Each spasm usually lasts less than 10 seconds. A cluster or severe spasms can last for minutes. After a spasm, the baby may cry or laugh. The spasms do not cause pain, but the baby may cry because the quick jerking movement surprises them.

Do babies cry when they have infantile spasms?

They might cry right before or right after they have a seizure. Your baby may also seem to twitch or jerk a muscle. You might hear the doctor call this myoclonus.