Quick Answer: What Is The Life Expectancy Of A Child With West Syndrome?

What do baby spasms look like?

What are infantile spasms.

Infantile spasms, sometimes called West syndrome, are a type of seizure that occurs in babies.

The spasms look like a sudden stiffening of muscles, and the baby’s arms, legs, or head may bend forward.

The seizures occur in a series of short spasms, about one to two seconds in length..

Does West syndrome go away?

West syndrome (also called infantile spasms) should go away by the time your child is 4 years old. But most people who had it will get another kind of epilepsy or seizure condition in childhood or as an adult. About 1 in 5 will have Lennox-Gastaut syndrome, a severe form of epilepsy with multiple types of seizures.

What is the cause of West syndrome?

Any disorder that can lead to brain damage can be an underlying cause of West syndrome including trauma, brain malformations such as hemimegalencephaly or cortical dysplasia, infections, chromosomal abnormalities such as Down syndrome, neurocutaneous disorders such as tuberous sclerosis complex (TSC), Sturge Weber …

Can you die from infantile spasms?

Infantile spasms is a complex and rare disorder that can have very serious consequences. It can lead to death in some babies, and cause intellectual disabilities and developmental problems in others. Even once the seizures are gone, the damaging brain effects can remain.

How common is West syndrome?

The combination of the infantile spasms, age of onset and EEG pattern defines the epilepsy syndrome called, ‘West syndrome’. It is called this after Dr William West, who first described the condition in his 4-month-old son in 1841. West syndrome happens in about one in 2,500-3,000 children.

What is the best treatment for infantile spasms?

Treatment of infantile spasms has little class I data, but adrenocorticotropic hormone (ACTH), prednisolone and vigabatrin have the best evidence as first-line medications. Other therapies including the ketogenic diet and other anti-epileptics medications may also prove useful in the treatment of infantile spasms.